A Case Report of Kussmaul-Maier Disease
DOI:
https://doi.org/10.31288/oftalmolzh201935256Keywords:
Kussmaul-Maier disease, periarteritis nodosaAbstract
Background: Kussmaul-Maier disease (also known as polyarteritis nodosa or PAN) is a systemic disorder characterized by destructive and proliferative changes in the walls of arteries (mainly muscular arteries and arterioles).
Purpose: To present a case exemplifying the ocular manifestations of Kussmaul-Maier disease.
Materials and Methods: The patient underwent visual acuity assessment, tonometry, and comprehensive eye examination. In addition, she underwent brain MRI and duplex sonography of the major arteries supplying the head.
Results and conclusion: This case demonstrates the features of disease course and ophthalmologist’s tactics in the treatment of Kussmaul-Maier disease. Kussmaul-Maier disease has a recurrent course with long-lasting (as long as 11 years) periods of remission and favorable visual prognosis.
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Copyright (c) 2025 О. О. Андрушкова, Н. В. Малачкова, К. Ю. Гріжимальська, Є. Г. Манько, Т. М. Жмудь
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